Autores: González Moreno Emmanuel I, Cámara Lemarroy Carlos Rodrigo, Borjas Almaguer David O, Martínez Cabriales Sylvia Aide, Paz Delgadillo Jonathan, Gutiérrez Udave Rodrigo, Ayala Cortés Ana Sofía, et al
Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
Palabras clave: Amyloid autoimmunity cholestasis pruritus.
2015-04-07 | 745 visitas | Evalua este artículo 0 valoraciones
Vol. 14 Núm.3. Mayo-Junio 2015 Pags. 416-419 Ann Hepatol 2015; 14(3)